Classification criteria for IgG4-RD

2019 American College of Rheumatology / European League Against Rheumatism classification criteria for IgG4-related disease¹

Step 1 - Entry criteria

Characteristic clinical or radiological involvement of a typical organ. Select all that apply.

Pancreas


Salivary glands


Bile ducts



Orbits


Kidney


Lung



Aorta




Retroperitoneum


Pachymeninges


Thyroid gland



Step 2 - Exclusion criteria

If at least one entry criterion is met, make sure that the patient meets none of the following items.



Clinical exclusion criteria


Serological exclusion criteria







Radiological exclusion criteria




Pathological exclusion criteria







Known diagnoses



Step 3 - Inclusion criteria

If no exclusion criterion is met, proceed to calculate this score. Only the highest weighted item in each domain is scored.

Histopathology




Immunostaining






Serum IgG4 concentration




Lacrimal and salivar glands (parotid, sublingual and submandibular)



Chest



Pancreas and biliary tree




Kidney




Retroperitoneum